DATASHEET
Formulation
white solid
Storage:
-20°C
Product Information:
Orally active ceramide-specific glycosyltransferase and α-glucosidase I and II inhibitor.1 Rescues trafficking-deficient F508del-CFTR in human airway epithelial cells via inhibition of ER α-glucosidases I and II.2 Pharmacological chaperone for glucocerebrosidase degradation.3 Clinically useful agent for Gaucher disease type 1.4 Stabilizes neurological disorders in Niemann-Pick disease type C.5
Description:
CAS Number: 210110-90-0<br></br>Chemical Name: N-Butyldeoxynojirimycin HCl<br></br>Molecular weight: 255.74<br></br>Formula: C10H21NO4 HCl<br></br>Solubility: DMSO (20 mg/ml) Water (20 mg/ml)<br></br>Physical Properties: White solid<br></br>Purity: 98% by TLC, NMR (Conforms)