bs-80506C [Life Science]
Miglustat HCl (N-Butyldeoxynojirimycin)
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DATASHEET

Formulation powder

Storage: -20°C

Product Information:

Molecular Weight:255.74

Formula:C10H21NO4 HCl

Purity:>98%

Solubility:Soluble in DMSO (up to 20 mg/ml) or in Water (up to 20 mg/ml).

Chemical Name:N-Butyldeoxynojirimycin HCl

Description:

Orally active ceramide-specific glycosyltransferase and α-glucosidase I and II inhibitor.1 Rescues trafficking-deficient F508del-CFTR in human airway epithelial cells via inhibition of ER α-glucosidases I and II.2 Pharmacological chaperone for glucocerebrosidase degradation.3 Clinically useful agent for Gaucher disease type 1.4 Stabilizes neurological disorders in Niemann-Pick disease type C.5

Size: 5 mg, 25 mg5 mg, 25 mg

Applications: Life Science()

For research use only. Not intended for diagnostic or therapeutic use.